Información de la revista
Vol. 115. Núm. 6.
Páginas T601 (junio 2024)
Compartir
Compartir
Descargar PDF
Más opciones de artículo
Vol. 115. Núm. 6.
Páginas T601 (junio 2024)
Images in Dermatology
Acceso a texto completo
Cannonball Pattern in a Tufted Angioma
Angioma en penacho, patrón en perdigonada
Visitas
1656
A. Giacamana,
Autor para correspondencia
anizagiacaman@gmail.com

Corresponding author.
, M.J. Beato Merinob, A. Martín-Santiagoa
a Departamento de Dermatología, Hospital Universitario Son Espases, Spain
b Departamento de Anatomía Patológica, Hospital Universitario La Paz, Spain
Contenido relacionado
Actas Dermosifiliogr. 2024;115:60110.1016/j.ad.2023.04.031
A. Giacaman, M.J. Beato Merino, A. Martín-Santiago
Este artículo ha recibido
Información del artículo
Texto completo
Descargar PDF
Estadísticas
Figuras (1)
Texto completo

A 3-year-old boy exhibited a congenital, erythematous-violaceous plaque with discreet hypertrichosis on his right thigh (Fig. 1A). Histopathological examination revealed the presence of fibrosis and lobules formed by capillaries on both the superficial and deep dermis, distributed in a “shotgun” pattern and surrounded by crescent moon-shaped vessels (Fig. 1B, HE ×10).

Figure 1
(0.08MB).

Since the first months of life, the patient had recurrent episodes of pain, increased local size and temperature, sometimes associated with fever and elevated acute phase reactants. Although the blood test results did not reveal the presence of thrombocytopenia or fibrinogen changes, they showed sustained elevation of D-dimer and hypogammaglobulinemia. The patient was treated with acetylsalicylic acid, ticlopidine, topical sirolimus, oral sirolimus, heparin, and oral corticosteroid cycles. Due to persistent pain and difficulty walking, surgical treatment was eventually performed.

Tufted angioma (TA) and kaposiform hemangioendothelioma are rare vascular tumors that fall within the same spectrum. In more than half of the cases, TA tends to resolve spontaneously. There are times, however, when it may present with pain and functional impairment, and even become complicated with the Kasabach-Merritt phenomenon, which means that patient monitoring is essential.

Funding

None declared.

Copyright © 2023. AEDV
Idiomas
Actas Dermo-Sifiliográficas
Opciones de artículo
Herramientas
es en

¿Es usted profesional sanitario apto para prescribir o dispensar medicamentos?

Are you a health professional able to prescribe or dispense drugs?