Journal Information
Vol. 89. Issue 9.
Pages 461-476 (September 1998)
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Vol. 89. Issue 9.
Pages 461-476 (September 1998)
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Diagnóstico, tratamiento y clasificación de la mastocitosis pediátrica. Estudio de 172 casos*
Diagnosis, management and classification of pediatric mastocytosis. A study of 172 cases.
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Antonio Torrelo Fernández, Lourdes Navarro Campoamor, Luis Escribano Mora, Antonio Zambrano Zambrano
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Fundamento: La mastocitosis en la infancia presenta unas características clínicas, patológicas y evolutivas diferentes a la mastocitosis del adulto. Existen pocas series amplias sobre mastocitosis pediátrica, y no se ha establecido con claridad un protocolo diagnóstico y terapéutico de la mastocitosis en la infancia. Tampoco existe un consenso de clasificación sobre esta enfermedad.
Palabras clave:
Mastocitosis
Pediatría
Mastocitoma
Urticaria pigmentosa
Background: Mastocytosis in children has distinctive features from adult mastocytosis. Few series have been published on pediatric mastocytosis, and diagnostic and therapeutic guidelines have not been clearly established. Finally, there is not a consensus classification of pediatric mastocytosis. Setting: A department of Dermatology from a Pediatric Hospital. Patients and methods: Between 1977 and 1997, 172 cases of mastocytosis were seen in children of less than 12 years old. Data from history and clinical examination were recorded. Basic hematologic and biochemical profile, radiologic skeletal survey and marrow aspirates with fine needle for microscopic study were obtained.
Keywords:
Mastocitosis
Pediatries
Mastocitoma
Urticaria pigmentosa
Idiomas
Actas Dermo-Sifiliográficas
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