Case Report of a Subcutaneous Peripheral Primitive Neuroectodermal Tumor

Cabrera, R.; Sánchez, P.; Rodríguez, M.A.

doi:10.1016/S1578-2190(08)70313-5

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We describe the case of a 45-year-old man with a subcutaneous peripheral primitive neuroectodermal tumor in which the t(11;22) translocation was detected. He was satisfactorily treated with surgery and radiotherapy." ] "es" => array:2 [ "titulo" => "Resumen" "resumen" => "La familia del tumor neuroectodérmico primitivo periférico/sarcoma de Ewing (PNET/ES) representa a un grupo de neoplasias malignas poco frecuentes, incluidas dentro de un grupo de tumores que presentan característicamente en su histología células redondas de pequeño tamaño. La traslocación 11;22 es típica de este tumor. Se presenta el caso de un varón de 45 años con un tumor subcutáneo neuroectodérmico primitivo periférico, en el que se detectó la traslocación t(11;22), tratado satisfactoriamente mediante cirugía y radioterapia." ] ] "bibliografia" => array:2 [ "titulo" => "References" "seccion" => array:1 [ 0 => array:1 [ "bibliografiaReferencia" => array:15 [ 0 => array:3 [ "identificador" => "bib1" "etiqueta" => "1." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Immunohistochemistry of small roundcell tumors" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "K. Devoe" 1 => "N. 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Abstract

Peripheral primitive neuroectodermal tumors—also known as Ewing sarcomas—are a rare type of malignant tumor the histology of which characteristically reveals the presence of small round cells. Typically, t(11;22) translocation is observed. We describe the case of a 45-year-old man with a subcutaneous peripheral primitive neuroectodermal tumor in which the t(11;22) translocation was detected. He was satisfactorily treated with surgery and radiotherapy.

Key words:

peripheral primitive neuroectodermal tumor

Resumen

La familia del tumor neuroectodérmico primitivo periférico/sarcoma de Ewing (PNET/ES) representa a un grupo de neoplasias malignas poco frecuentes, incluidas dentro de un grupo de tumores que presentan característicamente en su histología células redondas de pequeño tamaño. La traslocación 11;22 es típica de este tumor. Se presenta el caso de un varón de 45 años con un tumor subcutáneo neuroectodérmico primitivo periférico, en el que se detectó la traslocación t(11;22), tratado satisfactoriamente mediante cirugía y radioterapia.

Palabras clave:

tumor neuroectodérmico primitivo periférico

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References

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