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Vol. 109. Num. 5.June 2018
Pages e33-e36Pages 385-464
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Vol. 109. Num. 5.June 2018
Pages e33-e36Pages 385-464
e- Case Report
DOI: 10.1016/j.adengl.2018.04.005
Iso-Kikuchi Syndrome: Report of 3 Pediatric Cases
Síndrome de Iso-Kikuchi: 3 casos en la edad pediátrica
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L.L. Tirelli
Corresponding author
lucianatirelli@yahoo.com.ar

Corresponding author.
, P.C. Luna, R. Cano, J.P. Giraldo, M. Larralde
Servicio de Dermatología, Hospital Alemán, Ciudad Autónoma de Buenos Aires, Argentina
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Actas Dermosifiliogr 2018;109:38710.1016/j.adengl.2017.10.025
J. del Boz
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Abstract

Iso-Kikuchi syndrome, or congenital onychodysplasia of the index finger, is an uncommon condition characterized by total anonychia or dysplasia of the nail of the index finger. It is occasionally accompanied by underlying bone abnormalities and is rarely associated with other conditions. Although various hypotheses have been put forward to explain the pathophysiology of the syndrome, its etiology remains unknown.

We report the cases of 3 pediatric patients (2 boys and 1 girl) with nail changes and bone abnormalities consistent with Iso-Kikuchi syndrome. We highlight the importance of recognizing this entity early to avoid the need for additional tests and unnecessary treatment.

Keywords:
Iso-Kikuchi
Anonychia
Nail
Index finger
Phalanx
Resumen

El síndrome de Iso-Kikuchi, onicodisplasia congénita del dedo índice, es una entidad poco frecuente caracterizada por la anoniquia total o displasia de la uña del dedo índice, acompañado, en algunas ocasiones, de alteraciones óseas subyacentes, por lo general, en ausencia de otras anomalías. Si bien se han planteado distintas hipótesis fisiopatogénicas, la etiología sigue siendo desconocida.

Describimos los casos de 3 pacientes pediátricos, 2 varones y una niña, con alteraciones ungueales y óseas compatibles con el síndrome de Iso-Kikuchi. Destacamos la importancia de reconocer esta entidad tempranamente para evitar la realización de estudios complementarios y terapéuticas innecesarias.

Palabras clave:
Iso-Kikuchi
Anoniquia
Uña
Dedo índice
Falange

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